Niemann-Pick Disease Type C:Diagnosis and Outcome in Children, with Particular Reference to Liver disease
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Neuronal Intranuclear Inclusion Disease in a Child:Diagnosis by Rectal Biopsy
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A 30-Year-Old Woman Presenting with Rapidly Progressive Dementia and Extreme Hypoglycorrhachia
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A Woman With Multifocal Ischemic Strokes and Progressive Cognitive Impairment Due to Intravascular Lymphoma
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A Triad of Tremor, Ataxia, and Cognitive Impairment
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Clinicopathologic Conference, Cerebral Amyloid Angiopatny-Related Inflammation
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Chronic Meningitis
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A Rare Presentation of Whipple Disease
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A 42-year-old Woman with Progressive Cognitive Difficulties and Gait Imbalance
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Long Survival Sporadic Creutzfeldt-Jakob Disease
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Progressive Proximal Weakness in a 56-year-old Man with Bone Pain
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Neuronal Intranuclear Inclusion Disease Showing Intranuclear Inclusions in Renal Biopsy 12 Years Earlier
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Rapid Progression of Reversible Cognitive Impairment in an 80-year-old Man
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Clinicopathologic Conference, MELAS (mitochondrial encephalopathy, lactic acidosis, and stroke like episodes)
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Intractable Epilepsy and Progressive Cognitive Decline in a Young Man
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A New Potential Biomarker for Dementia with Lewy Bodies
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Validation of Clinicoradiological Criteria for the Diagnosis of Cerebral Amyloid Angiopathy-Related Inflammation
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Reversible Cognitive Decline Diagnosed on Ear Examination
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Neuronal Intranuclear Inclusion Disease Cases with Leukoencephalopathy Diagnosed via Skin Biopsy
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IgG4-Related Leptomeningitis: A Reversible Cause of Rapidly Progressive Cognitive Decline
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Amyloid Beta-Related Angiitis - A Case Report and Comprehensive Review of Literature of 94 Cases
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Progressive Neuropsychiatric Symptoms and Motor Impairment
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Central Nervous System Manifestation of IgG4-Related Disease
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Amyloid-Beta Related Angiitis of the Central Nervous System: Case Report and Topic Review
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A Case of Early-Onset Rapidly Progressive Dementia
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Infections of the Nervous System, (Bacterial, Fungal, Spirochetal, Parasitic) and Sarcoidosis, Whipple Disease
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Limbic Encephalitis as the Presenting Feature of Sj�gren Syndrome
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Expanding the Clinical, Radiological and Neuropathological Phenotype of Chronic Lymphocytic Inflammation with Pontine Perivascular Enhancement Responsive to Steroids (CLIPPERS)
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Cerebral Amyloid Angiopathy Related Inflammation: Three Case Reports and a Review
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The Evaluation of Rapidly Progressive Dementia
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Skin biopsy is useful for the antemortem diagnosis of neuronal intranuclear inclusion disease
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Cortical Restricted Diffusion as the Predominant MRI Finding in Sporadic Creutzfeldt-Jakob Disease
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Autoimmune Encephalopathy
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Brain Biopsy in Children With Primary Small-Vessel Central Nervous System Vasculitis
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Clinicopath Conf., Adult Cerebral Form of X-Linked Adrenoleukodystrophy
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A 23-Year-Old Man With Seizures and Visual Deficit
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Rapidly Progressive Dementia
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Stroke and Multi-Infarct Dementia as Presenting Symptoms of Giant Cell Arteritis: Report of 7 Cases and Review of the Literature
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Sporadic Adult-Onset Leukoencephalopathy with Neuroaxonal Spheroids Mimicking Cerebral MS
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Nonvasculitic Autoimmune Inflammatory Meningoencephalitis as a Cause of Potentially Reversible Dementia
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Primary Central Nervous System Vasculitis with Prominent Leptomeningeal Enhancement
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Whipples Disease
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A 34-Year-Old Man With Progressive Behavioral and Language Disturbance
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Cerebral Autosomal Dominant Arteriopathy With Subcortical Infarcts & Leukoencephalopathy (CADASIL)
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CT and MR Imaging of Neuroaxonal Leukodystrophy Presenting as Early-Onset Frontal Dementia
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Clinical Presentation and Pre-Mortem Diagnosis of Variant Creutzfeldt-Jakob Disease Associated With Blood Transfusion: A Case Report
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Vascular Parkinsonism and Dementia in a CADASIL Case with Intact Nigrostriatal Dopaminergic System
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Clinicopath Conf., MELAS Syndrome
NEJM 353:2271-2280, Case 36-2005, 2005
Neurological presentation of intravascular lymphoma: report of two cases and discussion of diagnostic challenges
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